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Elamipretide

Sharaxaad Gaaban:

Elamipretide waa tetrapeptide-mitochondria-bartilmaameed ah oo loo sameeyay in lagu daweeyo cudurrada ay keento cilladda mitochondrial, oo ay ku jiraan mitochondrial myopathy aasaasiga ah, Barth syndrome, iyo wadnaha oo shaqadiisa gabay.

 


Faahfaahinta Alaabta

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Elamipretide API

Elamipretide waa tetrapeptide-mitochondria-bartilmaameed ah oo loo sameeyay in lagu daweeyo cudurrada ay keento cilladda mitochondrial, oo ay ku jiraan mitochondrial myopathy aasaasiga ah, Barth syndrome, iyo wadnaha oo shaqadiisa gabay.

Farsamaynta & Cilmi-baarista:
Elamipretide waxay si xushmad leh u bartilmaameedsanaysaa cardiolipin ee xuubka mitochondrial gudaha, iyada oo hagaajinaysa:
Mitochondrial bioenergetics
Wax soo saarka ATP
Neefsashada gacanta iyo shaqada xubnaha

Waxay muujisay suurtagalnimada dib u soo celinta qaab-dhismeedka mitochondrial, yaraynta cadaadiska oksaydhka, iyo hagaajinta murqaha iyo waxqabadka wadnaha labadaba daraasadaha kiliinikada iyo kuwa horeba.


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