Elamipretide API
Elamipretide waa tetrapeptide-mitochondria-bartilmaameed ah oo loo sameeyay in lagu daweeyo cudurrada ay keento cilladda mitochondrial, oo ay ku jiraan mitochondrial myopathy aasaasiga ah, Barth syndrome, iyo wadnaha oo shaqadiisa gabay.
Farsamaynta & Cilmi-baarista:
Elamipretide waxay si xushmad leh u bartilmaameedsanaysaa cardiolipin ee xuubka mitochondrial gudaha, iyada oo hagaajinaysa:
Mitochondrial bioenergetics
Wax soo saarka ATP
Neefsashada gacanta iyo shaqada xubnaha
Waxay muujisay suurtagalnimada dib u soo celinta qaab-dhismeedka mitochondrial, yaraynta cadaadiska oksaydhka, iyo hagaajinta murqaha iyo waxqabadka wadnaha labadaba daraasadaha kiliinikada iyo kuwa horeba.